Thoas Fioretos
Research team manager
t(3;21)(q26;q22) with AML1 rearrangement in a de novo childhood acute monoblastic leukaemia
Author
Summary, in English
t(3;21)(q26;q22) is a recurrent chromosomal abnormality in Philadelphia-positive chronic myeloid leukaemia in blast crisis and in treatment-related myelodysplastic syndrome and acute myeloid leukaemia. The molecular consequences of the t(3;21) are presently being unravelled; various transcripts between the AML1 gene in 21q22 and several unrelated genes, i.e. EAP, EVI1 and MDS1, in 3q26 are generated, resulting in the formation of a chimaeric transcription factor. The t(3;21) has only rarely been described in de novo leukaemias and never before in an acute leukaemia in a child. We here present the clinical, cytogenetic and molecular genetic findings in a boy with a de novo acute monoblastic leukaemia with t(3;21)(q26;q22) and AML1 rearrangement.
Department/s
- Division of Clinical Genetics
- Paediatrics (Lund)
Publishing year
1996
Language
English
Pages
429-431
Publication/Series
British Journal of Haematology
Volume
92
Issue
2
Links
Document type
Journal article
Publisher
Wiley-Blackwell
Topic
- Hematology
Keywords
- childhood
- acute leukaemia
- translocation
- AML1
Status
Published
ISBN/ISSN/Other
- ISSN: 0007-1048